Pathology mcq on all topics combined helpful for mock testFull description
Pathology MCQs
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Pathology BONES, JOINTS, & SOFT-TISSUE TUMORS I.
Developmental Abnormalities a.
Malfomations and diseases caused by defects in nuclear proteins and transcription factors producing abnormalities in mesenchymal condensation and related cell differentiation: i. Synpolydactyl ii. Wardenburg syndrome iii. Greig syndrome iv. Campomelic dysplasia v. Oligodontia vi. Nail-patella syndrome vii. Holt-Oram Syndrome viii. Ulnar-mammary syndrome ix. Cleidocranial dysplasia
b. Diseases caused by defects in hormones and signal transduction mechanisms producing abnormal proliferation or maturation of chondrocytes i.
Brachdactylyl type C
ii. Jansen metaphyseal chondroplasia iii. Achondroplasia iv. Hypochondroplasia v. Thanotophoric dwarfism vi. Crouzon syndrome vii. Osteoporosis-pseudoglioma syndrome c.
Diseases associated with defects in extracellular structural proteins i. Type 1 Collagen Diseases 1. Osteogenesis imperfecta types I-IV (table 26-3) ii. Disease Associated with Mutations of Type 2, 9, 10, and 11 Collagen 1. Achondrogenesis II (type 2) 2. Hypochondrogenesis (type 2) 3. Stickler syndrome(type 2) 4. Multiple epiphyseal dysplasia (type 9) 5. Schmid metaphyseal chondrodysplasia (type 10)
d. Disease associated with defects in folding and degradation of macromolecules
Mucopolysaccharidoses
e. Disease associated with defects in Metabolic Pathways (enzymes, ion channels, and transporters)
f.
Disease associated with decreased bone mass
g.
Osteopetrosis Osteoporosis
Disease caused by osteoclast dysfunction i. Paget disease (Osteitis Deformans)
h. Disease associated with abnormal mineral homeostasis i. Rickets and osteomalacia ii. Hyerparathyoidism iii. Renal Osteodystrophy II.
Fractures
III.
Osteonecrosis (Avascular Necrosis)
IV.
Infections- Osteomylitis a.
Pyogenic osteomyelitis
b. Tuberculous osteomyelitis c. V.
Skeletal syphilis
Bone Tumors and Tumor-Like Lesions a.
Bone-Forming Tumors i. Osteoma ii. Osteoid Osteoma iii. Osteoblastoma iv. Osteosarcoma
b. Cartilage-Forming Tumors i. Osteochondroma ii. Chondromas iii. Chondroblastoma iv. Chondromyxoid Fibroma v. Chondrosarcoma c.
Fibrous and Fibro-osseous Tumors i. Fibrous Cortical Defect and Non-ossifying fibroma ii. Fibrous dysplasia iii. Fibrosarcoma variants
d. Miscellaneous Tumors i. Ewing Sarcoma/ Primitive Neuroectodermal Tumor ii. Giant Cell Tumor iii. Aneurysmal Bone Cyst iv. Metastatic disease VI.
Joints a.
Arthritis i. Osteoarthritis ii. Rheumatoid Arthritis iii. Juvenile Idiopathic arthritis iv. Seronegative Spondyloarthropathies 1. Ankylosing spondyloarthritis 2. Reiter Syndrome 3. Enteritis-associated arthritis 4. Psoriatic Arthritis v. Infectious Arthritis
1. Bacterial arthritis 2. Tuberculois Arthritis 3. Lyme Arthritis 4. Viral Arthritis vi. Crystal-Induced arthritis 1. Gout and gouty arthritis 2. Calcium pyrophosphate crystal deposition disease (pseudo-gout) b. Tumors and Tumor-like Lesions i. Ganglion and synovial Cyst ii. Tenosynovial Giant-cell tumor VII.
SOFT-TISSUE TUMORS AND TUMOR-LIKE LESIONS a.
Fatty Tumors i. Lipomas (mc soft-tissue tumor of adulthood) ii. Liposarcoma 1. Well-differentiated 2. Myxoid/round cell 3. Pleomorphic
b. Fibrous Tumors and Tumor-Like Lesions i. Reactive pseudosarcomatous proliferations 1. Nodular fasciitis 2. Myositis ossificans ii. Fibromatoses 1. Superficial Fibromatoses (palmar, plantar, penile fibromatoses) 2. Deep-seated Fibromatosis (desmoids tumors) c.
Fibrohistiocytic tumors i. Benign Fibrous histiocytoma (dermatofibroma) ii. Malignant fibrous histiocytoma
d. Tumors of Skeletal muscle i. Rhabdomyosarcoma e. Tumors of Smooth Muscle i. Leimyoma ii. Leiomyosarcoma f.
Synovial Sarcoma
a transcription factor (sometimes called a sequence-specific DNA-binding factor) is a protein that binds to specific DNA sequences, thereby controlling the movement (or transcription) of genetic information from DNA to mRNA. signal transduction is the process by which an extracellular signaling molecule activates a membrane receptor that in turn alters intracellular molecules creating a response. Mesenchyme, or mesenchymal connective tissue, is a type of undifferentiated loose connective tissue that is derived from all three germ layers and located within the embryo . Mesenchyme is characterized morphologically by a prominen t ground substance matrix containing a loose aggregate of reticular fibrils and unspecialized cells. The cells are capable of developing into connective tissues, such as bone, and cartilage, the lymphatic system, and the circulatory system.